A triad of deficient anterior abdominal wall underdevelopment, undescended testes and urinary tract anomalies characterizes the Prune Belly Syndrome (PBS). This is a very rare congenital malformation of uncertain etiology exclusive to males. Prenatal diagnosis of this syndrome is very important in its management and this is usually done during the mid-trimester ultrasound screening for fetal anomalies. We present a male neonate who had features suggestive of PBS prenatally, which were hydronephrosis, bilateral hydroureters and oligohydramnios. After delivery, these features were confirmed in addition to a lax anterior abdominal wall and a diagnosis of a severe form of Prune Belly Syndrome was made. Patient was managed conservatively but died eight days post-delivery.
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